Remodeling of skeletal muscle microvasculature in sickle cell trait and -thalassemia
نویسندگان
چکیده
Lucile Vincent, Léonard Féasson, Samuel Oyono-Enguéllé, Viviane Banimbek, Christian Denis, Catherine Guarneri, Emeline Aufradet, Géraldine Monchanin, Cyril Martin, David Gozal, Macias Dohbobga, Dieudonné Wouassi, Martin Garet, Patrice Thiriet, and Laurent Messonnier Laboratoire de Physiologie de l’Exercice, Université de Savoie, Chambéry; Institut Fédératif de Recherche en Sciences et Ingénierie de la Santé, Institut National de la Santé et de la Recherche Médicale, and Laboratoire de Physiologie de l’Exercice, Université Jean Monnet, and Unité de Myologie, Centre Hospitalier Universitaire de Saint Etienne, Saint Etienne, France; Laboratory of Physiology, Faculty of Medicine and Biomedical Sciences, University of Yaoundé I, Yaoundé, Cameroon; Centre de Recherche et d’Innovation sur le Sport, EA 647, Université Claude Bernard Lyon 1, Université de Lyon, Lyon, France; Department of Pediatrics, Pritzker School of Medicine, University of Chicago, Chicago, Illinois; and Institut National de la Jeunesse et des Sports, Yaoundé, Cameroon
منابع مشابه
Pre-marriage Sickle Cell Screening Program in South Region of Iran, A Pilot Study on 50 Cases of Sickle Trait
Background: Studies have demonstrated that sickle cell trait can be found in an asymptomatic healthy carrier with normal complete blood count (CBC) and red blood cell (RBC) indices. According to Iranian Ministry of Health bulletin instructions, prenuptial Thalassemia Screening Program (TSP) primarily depends on RBC indices which are measured through a routine CBC. Only when these levels are bel...
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Sickle cell-thalassemia associated with glucose- 6-phosphate dehydrogenese deficiency is reported in an Iranian family. The father had sickle trait and G.6.P.D. deficiency, the mother minor thalassemia, one of the sons siclc:le ceH-thailasemiia., the oth-er sickle cell trait; the daughter had sickle cell-thalassemia and was carrier of G.6.P.D. deficiellcy.
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Background: Approximately 180 mutations have been described in β-thalassemia worldwide with specific spectrum in each ethnic population. This study determines the spectrum and the frequency of β-thalassemia mutations in patients with β-thalassemia trait and sickle cell-β-thalassemia. Methods: Fifteen compound heterozygous sickle cell thalassemia (SCT) and 23 β-thalassemia trait patients were st...
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